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Posterior Polymorphous Corneal Dystrophy 1

Disease ID: disease_node_17146

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DbxrefICD10CM:H18.50, MIM:122000
SubclassofDOID_0050736, DOID_0060457
Data SourceDOID
SynonymsCHED1, Corneal Endothelial Dystrophy 1, Autosomal Dominant, Maumenee Corneal Dystrophy, PPCD1
Doid Labelposterior polymorphous corneal dystrophy 1
Doid DescriptionA posterior polymorphous corneal dystrophy that has_material_basis_in autosomal domit inheritance of mutation in the OVOL2 gene on chromosome 20p11.23.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_17146
Doid IdDOID_0110855
LabelPosterior Polymorphous Corneal Dystrophy 1