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Autosomal Recessive Cutis Laxa Type Iib

Disease ID: disease_node_17139

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DbxrefICD10CM:Q82.8, MIM:612940, ORDO:357064
SubclassofDOID_3144, DOID_0050737
Data SourceDOID
SynonymsARCL2, progeroid type, ARCL2B
Doid Labelautosomal recessive cutis laxa type IIB
Doid DescriptionA cutis laxa characterized by progeroid features that has_material_basis_in homozygous or compound heterozygous mutation in the PYCR1 gene on chromosome 17q25.3.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17139
Doid IdDOID_0070137
LabelAutosomal Recessive Cutis Laxa Type Iib