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Autosomal Recessive Cutis Laxa Type Ii Classic Type

Disease ID: disease_node_17135

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DbxrefICD10CM:Q82.8, ORDO:357074
SubclassofDOID_0050737, DOID_3144
Data SourceDOID
SynonymsARCL2, Debre type, ARCL2, classic type
Doid Labelautosomal recessive cutis laxa type II classic type
Doid DescriptionA cutis laxa characterized by generalized skin wrinkling, sparse subcutaneous fat, dysmorphic progeroid facial features and severe hypotonia.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17135
Doid IdDOID_0070141
LabelAutosomal Recessive Cutis Laxa Type Ii Classic Type