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Autosomal Domit Cutis Laxa 3

Disease ID: disease_node_17133

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DbxrefICD10CM:Q82.8, MIM:616603
SubclassofDOID_0070142
Data SourceDOID
SynonymsADCL3
Doid Labelautosomal domit cutis laxa 3
Doid DescriptionAn autosomal domit cutis laxa characterized by thin skin with visible veins and wrinkles, cataract or corneal clouding, clenched fingers, pre- and postnatal growth retardation, moderate intellectual disability, and a combination of muscle hypotonia with brisk muscle reflexes that has_material_basis_in heterozygous mutation in the ALDH18A1 gene on chromosome 10q24.
Disease Node Iddisease_node_17133
Doid IdDOID_0070131
LabelAutosomal Domit Cutis Laxa 3