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Primary Localized Cutaneous Amyloidosis 3

Disease ID: disease_node_17124

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DbxrefMIM:617920
SubclassofDOID_0050639
Data SourceDOID
SynonymsAmyloidosis cutis dyschromica
Doid Labelprimary localized cutaneous amyloidosis 3
Doid DescriptionA primary cutaneous amyloidosis that is characterized by deposits of keratinocyte-derived amyloid in the skin and that has_material_basis_in homozygous or compound heterozygous mutation in the GPNMB gene on chromosome 7p15. Onset occurs before puberty and involves macular or reticulate hyperpigmentation admixed with symmetrically distributed guttate hypopigmented and hyperpigmented lesions.
Disease Node Iddisease_node_17124
Doid IdDOID_0080932
LabelPrimary Localized Cutaneous Amyloidosis 3