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Bernard-Soulier Syndrome Type A2

Disease ID: disease_node_17066

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DbxrefMIM:153670
SubclassofDOID_2217
Data SourceDOID
SynonymsBSSA2
Doid LabelBernard-Soulier syndrome type A2
Doid DescriptionA Bernard-Soulier syndrome characterized by autosomal domit inheritance of mild to moderate bleeding tendency, thrombocytopenia, and an increased mean platelet size that has_material_basis_in heterozygous mutations in the GP1BA gene on chromosome 17p.
Has SymptomSYMP_0000007
Disease Node Iddisease_node_17066
Doid IdDOID_0111059
LabelBernard-Soulier Syndrome Type A2