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Autosomal Domit Robinow Syndrome 2

Disease ID: disease_node_17029

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DbxrefMIM:616331, ORDO:3107
SubclassofDOID_0050736, DOID_0060254
Data SourceDOID
SynonymsDRS2
Doid Labelautosomal domit Robinow syndrome 2
Doid DescriptionA Robinow syndrome characterized by autosomal domit inheritance of mesomelic limb shortening, genital hypoplasia, and distinctive facial features that has_material_basis_in heterozygous mutation in the DVL1 gene on chromosome 1p36.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_17029
Doid IdDOID_0060765
LabelAutosomal Domit Robinow Syndrome 2