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Primary Coenzyme Q10 Deficiency 2

Disease ID: disease_node_17022

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DbxrefMIM:614651, ORDO:254898
SubclassofDOID_0050730
Data SourceDOID
SynonymsCOQ10D2, coenzyme Q10 deficiency, primary, 2, deafness-encephaloneuropathy-obesity-valvulopathy syndrome, hearing loss-encephaloneuropathy-obesity-valvulopathy syndrome
Doid Labelprimary coenzyme Q10 deficiency 2
Doid DescriptionA primary coenzyme Q10 deficiency that has_material_basis_in an autosomal recessive mutation of the PDSS1 gene on chromosome 10p12.1.
Disease Node Iddisease_node_17022
Doid IdDOID_0070239
Disease Has Basis InSO_0001537
LabelPrimary Coenzyme Q10 Deficiency 2