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Primary Coenzyme Q10 Deficiency 5

Disease ID: disease_node_17019

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DbxrefMIM:614654, ORDO:319678
SubclassofDOID_0050730
Data SourceDOID
SynonymsCOQ10D5, coenzyme Q10 deficiency, primary, 5, encephalopathy-hypertrophic cardiomyopathy-renal tubular disease syndrome
Doid Labelprimary coenzyme Q10 deficiency 5
Doid DescriptionA primary coenzyme Q10 deficiency that has_material_basis_in an autosomal recessive mutation of the COQ9 gene on chromosome 16q21.
Disease Node Iddisease_node_17019
Doid IdDOID_0070242
Disease Has Basis InSO_0001537
LabelPrimary Coenzyme Q10 Deficiency 5