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Multiple Congenital Anomalies-Hypotonia-Seizures Syndrome 4

Disease ID: disease_node_16970

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DbxrefMIM:618548
SubclassofDOID_0080503, DOID_0050737
Data SourceDOID
SynonymsDEE77, GPIBD19, MCAHS4, developmental and epileptic encephalopathy 77, early infantile epileptic encephalopathy 77, glycosylphosphatidylinositol biosynthesis defect 19
Doid Labelmultiple congenital anomalies-hypotonia-seizures syndrome 4
Doid DescriptionA multiple congenital anomalies-hypotonia-seizures syndrome characterized by onset in the first months of life of refractory seizures and severe global developmental delay that has_material_basis_in homozygous or compound heterozygous mutation in the PIGQ gene on chromosome 16p13.3.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16970
Doid IdDOID_0112213
LabelMultiple Congenital Anomalies-Hypotonia-Seizures Syndrome 4