This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Familial Hyperinsulinemic Hypoglycemia 3

Disease ID: disease_node_16858

Connections displayed (default: 10).
Loading graph...

DbxrefGARD:2818, MIM:602485, ORDO:79299
SubclassofDOID_0050736, DOID_13317
Data SourceDOID
SynonymsHHF3, hyperinsulinemic hypoglycemia due to glucokinase deficiency, hyperinsulinism due to glucokinase deficiency
Doid Labelfamilial hyperinsulinemic hypoglycemia 3
Doid DescriptionA hyperinsulinemic hypoglycemia characterized by autosomal domit inheritance of a reduced threshold for insulin release and hypoglycemia induced by fasting or protein rich meals that has_material_basis_in activating mutations in the GCK gene on chromosome 7p13.
Has PhenotypeHP_0011015
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_16858
Doid IdDOID_0070216
LabelFamilial Hyperinsulinemic Hypoglycemia 3