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Familial Hyperinsulinemic Hypoglycemia 1

Disease ID: disease_node_16855

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DbxrefMIM:256450
SubclassofDOID_0050736, DOID_0050737, DOID_13317
Data SourceDOID
SynonymsHHF1
Doid Labelfamilial hyperinsulinemic hypoglycemia 1
Doid DescriptionA hyperinsulinemic hypoglycemia characterized by autosomal recessive inheritance of hyperinsulinemic hypoglycemia that is resistant to diazoxide treatment that has_material_basis_in mutation in the ABCC8 gene on chromosome 11p15.
Has PhenotypeHP_0011015
Has Material Basis InGENO_0000147, GENO_0000148
Disease Node Iddisease_node_16855
Doid IdDOID_0070219
LabelFamilial Hyperinsulinemic Hypoglycemia 1