This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Familial Gpihbp1 Deficiency

Disease ID: disease_node_16848

Connections displayed (default: 10).
Loading graph...

DbxrefMIM:615947, ORDO:535458
SubclassofDOID_0050737, DOID_0111417
Data SourceDOID
Synonymsfamilial glycosylphosphatidylinositol-anchored high density lipoprotein-binding protein 1 deficiency, hyperlipoproteinemia type 1D, hyperlipoproteinemia type ID
Doid Labelfamilial GPIHBP1 deficiency
Doid DescriptionA familial chylomicronemia syndrome characterized by refactory fasting hyperchylomicronemia, and elevated plasma triglyceride levels that has_material_basis_in homozygous or compound heterozygous mutation in the GPIHBP1 gene on chromosome 8q24.3.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16848
Doid IdDOID_0111420
LabelFamilial Gpihbp1 Deficiency