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Mitochondrial Dna Depletion Syndrome 17

Disease ID: disease_node_16829

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DbxrefMIM:618567
SubclassofDOID_0050737, DOID_0070329
Data SourceDOID
Doid Labelmitochondrial DNA depletion syndrome 17
Doid DescriptionA mitochondrial DNA depletion syndrome characterized by childhood onset of encephalopathy, stroke-like episodes, lactic acidosis, hypocitrullinemia, and multiple mitochondrial oxidative phosphorylation deficiencies that has_material_basis_in homozygous mutation in the MRM2 gene on chromosome 7p22.3. Phenotype is similar to MELAS syndrome.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16829
Doid IdDOID_0070448
LabelMitochondrial Dna Depletion Syndrome 17