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Mitochondrial Dna Depletion Syndrome 18

Disease ID: disease_node_16828

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DbxrefMIM:618811
SubclassofDOID_0050737, DOID_0070329
Data SourceDOID
Doid Labelmitochondrial DNA depletion syndrome 18
Doid DescriptionA mitochondrial DNA depletion syndrome characterized by early onset progressive weakness, atrophy of the distal limb muscles, and multiple mitochondrial oxidative phosphorylation deficiencies that has_material_basis_in homozygous mutation in the SLC25A21 gene on chromosome 14q11.3.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16828
Doid IdDOID_0070449
LabelMitochondrial Dna Depletion Syndrome 18