This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Mitochondrial Dna Depletion Syndrome 14

Disease ID: disease_node_16820

Connections displayed (default: 10).
Loading graph...

DbxrefMIM:616896
SubclassofDOID_0070329
Data SourceDOID
Doid Labelmitochondrial DNA depletion syndrome 14
Doid DescriptionA mitochondrial DNA depletion syndrome that is characterized by severe lethal infantile mitochondrial encephalomyopathy and hypertrophic cardiomyopathy, with hypotonia and peripheral hypertonia with opisthotonic posturing, as well as feeding difficulties and profound neurodevelopmental delay, and has_material_basis_in homozygous mutation in the OPA1 mitochondrial dynamin like GTPase gene on chromosome 3q29.
Has PhenotypeHP_0012758
Disease Node Iddisease_node_16820
Doid IdDOID_0080336
LabelMitochondrial Dna Depletion Syndrome 14