This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Multiple Mitochondrial Dysfunctions Syndrome 1

Disease ID: disease_node_16815

Connections displayed (default: 10).
Loading graph...

DbxrefGARD:12632, MIM:605711, ORDO:401869
SubclassofDOID_0050737, DOID_0070330
Data SourceDOID
SynonymsNFU1 deficiency
Doid Labelmultiple mitochondrial dysfunctions syndrome 1
Doid DescriptionA multiple mitochondrial dysfunctions syndrome that is characterized by weakness, respiratory failure, lack of neurologic development, lactic acidosis, and early death, and has_material_basis_in autosomal recessive inheritance of homozygous or compound heterozygous mutation in the NFU1 iron-sulfur cluster scaffold gene on chromosome 2p13.
Has SymptomSYMP_0000094
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16815
Doid IdDOID_0080133
LabelMultiple Mitochondrial Dysfunctions Syndrome 1