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Mitochondrial Complex V (Atp Synthase) Deficiency Nuclear Type 4B

Disease ID: disease_node_16797

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DbxrefMIM:615228
SubclassofDOID_0060333, DOID_0050737
Data SourceDOID
SynonymsMC5DN4B
Doid Labelmitochondrial complex V (ATP synthase) deficiency nuclear type 4B
Doid DescriptionA mitochondrial complex V (ATP synthase) deficiency nuclear type 4 characterized by onset at birth of horizontal and vertical nystagmus, abnormal primitive reflexes, and tonus dysregulation, followed by fatal encephalopathy that has_material_basis_in autosomal recessive inheritance.
Existence Starts DuringHP_0003577
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16797
Doid IdDOID_0070462
LabelMitochondrial Complex V (Atp Synthase) Deficiency Nuclear Type 4B