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Cox Deficiency, Infantile Mitochondrial Myopathy

Disease ID: disease_node_16785

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DbxrefORDO:1561, UMLS_CUI:C4273730
SubclassofDOID_3762
Data SourceDOID
Synonymscardioencephalomyopathy, fatal infantile, due to cytochrome c oxidase deficiency, fatal infantile COX deficiency, fatal infantile cardioencephalomyopathy due to cytochrome c oxidase deficiency, fatal infantile cytochrome C oxidase deficiency, fatal infantile encephalocardiomyopathy
Doid LabelCOX deficiency, infantile mitochondrial myopathy
Doid DescriptionA cytochrome-c oxidase deficiency disease characterized by myotonia, abnormalities of the heart and kidneys, and lactic acidosis. Xref MGI.
Disease Node Iddisease_node_16785
Doid IdDOID_0050713
LabelCox Deficiency, Infantile Mitochondrial Myopathy