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Combined Oxidative Phosphorylation Deficiency 56

Disease ID: disease_node_16761

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DbxrefMIM:620139
SubclassofDOID_0050737, DOID_0060286
Data SourceDOID
SynonymsCOXPD56
Doid Labelcombined oxidative phosphorylation deficiency 56
Doid DescriptionA combined oxidative phosphorylation deficiency characterized by lethargy at birth, hypotonia, developmental delay, myopathy, and ptosis that has_material_basis_in compound heterozygous mutation in the TAMM41 gene on chromosome 3p25.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16761
Doid IdDOID_0070429
LabelCombined Oxidative Phosphorylation Deficiency 56