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Combined Oxidative Phosphorylation Deficiency 35

Disease ID: disease_node_16759

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DbxrefMIM:617873
SubclassofDOID_0050737, DOID_0060286
Data SourceDOID
SynonymsCOXPD35
Doid Labelcombined oxidative phosphorylation deficiency 35
Doid DescriptionA combined oxidative phosphorylation deficiency characterized by global developmental delay with intellectual disability, microcephaly, and early-onset seizures that has_material_basis_in homozygous or compound heterozygous mutation in the TRIT1 gene on chromosome 1p34.2.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16759
Doid IdDOID_0111464
LabelCombined Oxidative Phosphorylation Deficiency 35