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Combined Oxidative Phosphorylation Deficiency 19

Disease ID: disease_node_16749

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DbxrefMIM:615595, ORDO:397593
SubclassofDOID_0050737, DOID_0060286
Data SourceDOID
SynonymsCOXPD19, severe neonatal lactic acidosis due to NFS1-ISD11 complex deficiency
Doid Labelcombined oxidative phosphorylation deficiency 19
Doid DescriptionA combined oxidative phosphorylation deficiency that has_material_basis_in homozygous or compound heterozygous mutation in the LYRM4 gene on chromosome 6p25.1.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16749
Doid IdDOID_0111476
LabelCombined Oxidative Phosphorylation Deficiency 19