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Combined Oxidative Phosphorylation Deficiency 14

Disease ID: disease_node_16748

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DbxrefMIM:614946, ORDO:319519
SubclassofDOID_0050737, DOID_0060286
Data SourceDOID
SynonymsCOXPD14
Doid Labelcombined oxidative phosphorylation deficiency 14
Doid DescriptionA combined oxidative phosphorylation deficiency characterized by neonatal onset of global developmental delay, refractory seizures, and lactic acidosis that has_material_basis_in homozygous or compound heterozygous mutation in the FARS2 gene on chromosome 6p25.1.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16748
Doid IdDOID_0111477
LabelCombined Oxidative Phosphorylation Deficiency 14