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Combined Oxidative Phosphorylation Deficiency 10

Disease ID: disease_node_16745

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DbxrefMIM:614702, ORDO:314637
SubclassofDOID_0050737, DOID_0060286
Data SourceDOID
SynonymsCOXPD10, infantile hypertrophic mitochondrial cardiomyopathy and lactic acidosis, mitochondrial hypertrophic cardiomyopathy with lactic acidosis due to MTO1 deficiency
Doid Labelcombined oxidative phosphorylation deficiency 10
Doid DescriptionA combined oxidative phosphorylation deficiency characterized by hypertrophic cardiomyopathy and lactic acidosis that has_material_basis_in homozygous or compound heterozygous mutation in the MTO1 gene on chromosome 6q13.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16745
Doid IdDOID_0111480
LabelCombined Oxidative Phosphorylation Deficiency 10