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Combined Oxidative Phosphorylation Deficiency 11

Disease ID: disease_node_16744

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DbxrefMIM:614922, ORDO:324535
SubclassofDOID_0050737, DOID_0060286
Data SourceDOID
SynonymsCOXPD11, infantile encephaloneuromyopathy due to mitochondrial translation defect
Doid Labelcombined oxidative phosphorylation deficiency 11
Doid DescriptionA combined oxidative phosphorylation deficiency characterized by neonatal hypotonia, lactic acidosis, death in infancy and in some cases respiratory insufficiency, foot deformities, or seizures that has_material_basis_in homozygous or compound heterozygous mutation in the RMND1 gene on chromosome 6q25.1.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16744
Doid IdDOID_0111481
LabelCombined Oxidative Phosphorylation Deficiency 11