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Combined Oxidative Phosphorylation Deficiency 31

Disease ID: disease_node_16739

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DbxrefMIM:617228, ORDO:478049
SubclassofDOID_0050737, DOID_0060286
Data SourceDOID
SynonymsCOXPD31, lethal left ventricular non-compaction-seizures-hypotonia-cataract-developmental delay syndrome
Doid Labelcombined oxidative phosphorylation deficiency 31
Doid DescriptionA combined oxidative phosphorylation deficiency characterized by global developmental delay, severe hypotonia, and left ventricular non-compaction that has_material_basis_in homozygous or compound heterozygous mutation in the MIPEP gene on chromosome 13q12.12.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16739
Doid IdDOID_0111488
LabelCombined Oxidative Phosphorylation Deficiency 31