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Combined Oxidative Phosphorylation Deficiency 23

Disease ID: disease_node_16728

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DbxrefMIM:616198, ORDO:444013
SubclassofDOID_0050737, DOID_0060286
Data SourceDOID
SynonymsCOXPD23
Doid Labelcombined oxidative phosphorylation deficiency 23
Doid DescriptionA combined oxidative phosphorylation deficiency characterized by early childhood onset of hypertrophic cardiomyopathy and/or neurologic symptoms, including hypotonia and delayed psychomotor development that has_material_basis_in homozygous or compound heterozygous mutation in the GTPBP3 gene on chromosome 19p13.11.
Has SymptomSYMP_0020049
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16728
Doid IdDOID_0111500
LabelCombined Oxidative Phosphorylation Deficiency 23