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Combined Oxidative Phosphorylation Deficiency 6

Disease ID: disease_node_16726

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DbxrefMIM:300816, ORDO:238329
SubclassofDOID_0080012, DOID_0060286
Data SourceDOID
SynonymsCOXPD6, Mitochondrial encephalomyopathy due to COXPD6, Mitochondrial encephalomyopathy due to combined oxidative phosphorylation defect 6, severe X-linked mitochondrial encephalomyopathy
Doid Labelcombined oxidative phosphorylation deficiency 6
Doid DescriptionA combined oxidative phosphorylation deficiency that has_material_basis_in hemizygous mutation in the AIFM1 gene on chromosome Xq26.1.
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_16726
Doid IdDOID_0111502
LabelCombined Oxidative Phosphorylation Deficiency 6