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Hereditary Spastic Paraplegia 39

Disease ID: disease_node_16689

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DbxrefGARD:4924, ICD10CM:G11.4, MIM:612020, ORDO:139480
SubclassofDOID_2476, DOID_0050737
Data SourceDOID
SynonymsNTE-related motor neuron disorder, NTEMND, SPG39, autosomal recessive spastic paraplegia 39, autosomal recessive spastic paraplegia type 39, spastic paraplegia due to NTE mutation, spastic paraplegia due to neuropathy target esterase mutation
Doid Labelhereditary spastic paraplegia 39
Doid DescriptionA hereditary spastic paraplegia that has_material_basis_in mutation in the PNPLA6 gene on chromosome 19p13.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16689
Doid IdDOID_0110790
LabelHereditary Spastic Paraplegia 39