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Hereditary Spastic Paraplegia 5A

Disease ID: disease_node_16661

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DbxrefGARD:4926, ICD10CM:G11.4, MIM:270800, ORDO:100986
SubclassofDOID_2476, DOID_0050737
Data SourceDOID
SynonymsSPG5A, autosomal recessive spastic paraplegia 5A, autosomal recessive spastic paraplegia type 5A
Doid Labelhereditary spastic paraplegia 5A
Doid DescriptionA hereditary spastic paraplegia that is characterized by progressive muscle weakness and paraplegia and has_material_basis_in mutation in the CYP7B1 gene on chromosome 8q12.
Has SymptomSYMP_0000363, SYMP_0000094
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16661
Doid IdDOID_0110810
LabelHereditary Spastic Paraplegia 5A