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Progressive Myoclonus Epilepsy 6

Disease ID: disease_node_16297

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DbxrefGARD:3872, MIM:614018, ORDO:280620
SubclassofDOID_891, DOID_0050737
Data SourceDOID
SynonymsEPM6, GOSR2-related progressive myoclonus ataxia, North Sea progressive myoclonus epilepsy, PME type 6, Progressive myoclonus epilepsy type 6
Doid Labelprogressive myoclonus epilepsy 6
Doid DescriptionA progressive myoclonus epilepsy characterized by onset of ataxia in the first years of life, followed by action myoclonus and seizures later in childhood, and loss of independent ambulation in the second decade that has_material_basis_in homozygous or compound heterozygous mutation in the GOSR2 gene on chromosome 17q21.32.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16297
Doid IdDOID_0111449
LabelProgressive Myoclonus Epilepsy 6