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Progressive Myoclonus Epilepsy 1A

Disease ID: disease_node_16293

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DbxrefMIM:254800
SubclassofDOID_3535, DOID_0050737
Data SourceDOID
SynonymsEPM1A
Doid Labelprogressive myoclonus epilepsy 1A
Doid DescriptionAn Unverricht-Lundborg syndrome that has_material_basis_in homozygous or compound heterozygous in the CSTB gene on chromosome 21q22.3.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16293
Doid IdDOID_0111452
LabelProgressive Myoclonus Epilepsy 1A