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Familial Adult Myoclonic Epilepsy 5

Disease ID: disease_node_16288

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DbxrefMIM:615400
SubclassofDOID_0050737, DOID_0111689
Data SourceDOID
SynonymsFAME5, FCMTE5, familial cortical myoclonic tremor and epilepsy 5
Doid Labelfamilial adult myoclonic epilepsy 5
Doid DescriptionA familial adult myoclonic epilepsy characterized by onset of seizures in adolescence, followed by the development of cortical myoclonic tremor that has_material_basis_in homozygous or compound heterozygous mutation in the CNTN2 gene on chromosome 1q32.1.
Existence Starts DuringHP_0003581
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16288
Doid IdDOID_0111691
LabelFamilial Adult Myoclonic Epilepsy 5