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Familial Adult Myoclonic Epilepsy 2

Disease ID: disease_node_16287

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DbxrefMIM:607876
SubclassofDOID_0050736, DOID_0111689
Data SourceDOID
SynonymsADCME, BAFME2, FAME2, FCMTE2, autosomal dominant cortical myoclonus and epilepsy, benign adult familial myoclonic epilepsy 2, familial cortical myoclonic tremor and epilepsy 2
Doid Labelfamilial adult myoclonic epilepsy 2
Doid DescriptionA familial adult myoclonic epilepsy characterized by onset of tremor affecting the fingers, hand, and voice in adolescence or young adulthood with somewhat later onset of rhythmic myoclonic jerks and generalized tonic-clonic seizures that has_material_basis_in a heterozygous 5-bp repeat expansion in STARD7 on chromosome 2q11.2.
Existence Starts DuringHP_0003581
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_16287
Doid IdDOID_0111692
LabelFamilial Adult Myoclonic Epilepsy 2