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Developmental And Epileptic Encephalopathy 71

Disease ID: disease_node_16181

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DbxrefMIM:618328
SubclassofDOID_0050737, DOID_0112202
Data SourceDOID
SynonymsDEE71, early infantile epileptic encephalopathy 71, glutaminase deficiency with neonatal epileptic encephalopathy
Doid Labeldevelopmental and epileptic encephalopathy 71
Doid DescriptionA developmental and epileptic encephalopathy characterized by early neonatal refractory seizures, respiratory failure, structural brain abnormalities and cerebral edema, with death within weeks after birth that has_material_basis_in homozygous or compound heterozygous mutation in GLS on chromosome 2q32.2.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16181
Doid IdDOID_0112207
LabelDevelopmental And Epileptic Encephalopathy 71