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Bilateral Parasagittal Parieto-Occipital Polymicrogyria

Disease ID: disease_node_16160

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DbxrefGARD:10785, MIM:612691, ORDO:208441
SubclassofDOID_0050737, DOID_0080918
Data SourceDOID
Synonymsbilateral temporooccipital polymicrogyria
Doid Labelbilateral parasagittal parieto-occipital polymicrogyria
Doid DescriptionA polymicrogyria that is characterized by bilateral malformation of cortical development, centered around the parasagittal and mesial aspects of the parietooccipital cortex and that has_material_basis_in homozygous mutation in the FIG4 gene on chromosome 6q21.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16160
Doid IdDOID_0080923
LabelBilateral Parasagittal Parieto-Occipital Polymicrogyria