This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Pontocerebellar Hypoplasia Type 1A

Disease ID: disease_node_16117

Connections displayed (default: 10).
Loading graph...

DbxrefMIM:607596, ORDO:2254
SubclassofDOID_0112322, DOID_0050737
Data SourceDOID
Doid Labelpontocerebellar hypoplasia type 1A
Doid DescriptionA pontocerebellar hypoplasia that is characterized by central and peripheral motor dysfunction, hypotonia, spasticity and failure to thrive, has_material_basis_in homozygous or compound heterozygous mutation in the VRK1 gene. NT MGI.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16117
Doid IdDOID_0060265
LabelPontocerebellar Hypoplasia Type 1A