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Pontocerebellar Hypoplasia Type 1B

Disease ID: disease_node_16116

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DbxrefMIM:614678, ORDO:2254
SubclassofDOID_0112322, DOID_0050737
Data SourceDOID
Doid Labelpontocerebellar hypoplasia type 1B
Doid DescriptionA severe pontocerebellar hypoplasia that is characterized by hypotonia, progressive microcephaly and developmental delay, has_material_basis_in autosomal recessive inheritance of mutation in the EXOSC3 gene. NT MGI.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16116
Doid IdDOID_0060266
LabelPontocerebellar Hypoplasia Type 1B