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Pontocerebellar Hypoplasia Type 1D

Disease ID: disease_node_16115

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DbxrefMIM:618065
SubclassofDOID_0112322, DOID_0050737
Data SourceDOID
SynonymsPCH1D
Doid Labelpontocerebellar hypoplasia type 1D
Doid DescriptionA pontocerebellar hypoplasia type 1 characterized by severe hypotonia and motor neuronopathy detectable at birth or in infancy that has_material_basis_in homozygous or compound heterozygous mutation in the EXOSC9 gene on chromosome 4q27.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16115
Doid IdDOID_0112323
LabelPontocerebellar Hypoplasia Type 1D