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Pontocerebellar Hypoplasia Type 1C

Disease ID: disease_node_16112

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DbxrefMIM:616081
SubclassofDOID_0112322, DOID_0050737
Data SourceDOID
SynonymsPCH1C
Doid Labelpontocerebellar hypoplasia type 1C
Doid DescriptionA pontocerebellar hypoplasia type 1 characterized by severe muscle weakness and failure to thrive apparent in the first months of life that has_material_basis_in homozygous or compound heterozygous mutation in the EXOSC8 gene on chromosome 13q13.3.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16112
Doid IdDOID_0112334
LabelPontocerebellar Hypoplasia Type 1C