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Pontocerebellar Hypoplasia Type 2E

Disease ID: disease_node_16106

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DbxrefMIM:615851
SubclassofDOID_0050737, DOID_0112328
Data SourceDOID
Doid Labelpontocerebellar hypoplasia type 2E
Doid DescriptionA pontocerebellar hypoplasia that is characterized by progressive microcephaly, profound intellectual disability, spasticity and seizure, has_material_basis_in autosomal recessive inheritance of mutation in the VPS53 gene. NT MGI.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_16106
Doid IdDOID_0060271
LabelPontocerebellar Hypoplasia Type 2E