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Neuronal Intranuclear Inclusion Disease

Disease ID: disease_node_16099

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DbxrefMIM:603472
SubclassofDOID_0050736, DOID_1289
Data SourceDOID
Doid Labelneuronal intranuclear inclusion disease
Doid DescriptionA neurodegenerative disease that is characterized by a wide range of clinical manifestations, including pyramidal and extrapyramidal symptoms, cerebellar ataxia, cognitive decline and dementia, peripheral neuropathy, and autonomic dysfunction, and that has_material_basis_in heterozygous repeat expansion (CGG) in the 5-prime untranslated region of the NOTCH2NLC gene on chromosome 1q21.
Has Material Basis InGENO_0000147, SO_0002165
Disease Node Iddisease_node_16099
Doid IdDOID_0081294
LabelNeuronal Intranuclear Inclusion Disease