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Autosomal Recessive Spinocerebellar Ataxia 23

Disease ID: disease_node_16012

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DbxrefMIM:616949, ORDO:404493
SubclassofDOID_0050950
Data SourceDOID
SynonymsSCAR23, autosomal recessive cerebellar ataxia-epilepsy-intellectual disability syndrome due to TUD deficiency
Doid Labelautosomal recessive spinocerebellar ataxia 23
Doid DescriptionAn autosomal recessive cerebellar ataxia characterized by epilepsy, intellectual disability, and gait ataxia that has_material_basis_in homozygous or compound heterozygous mutation in the TDP2 gene on chromosome 6p22.3.
Disease Node Iddisease_node_16012
Doid IdDOID_0111613
LabelAutosomal Recessive Spinocerebellar Ataxia 23