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Neuronal Ceroid Lipofuscinosis 13

Disease ID: disease_node_15958

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DbxrefICD10CM:E75.4, MIM:615362, ORDO:352709
SubclassofDOID_0050737, DOID_14503
Data SourceDOID
SynonymsCLN13, neuronal ceroid lipofuscinosis 13 Kufs type
Doid Labelneuronal ceroid lipofuscinosis 13
Doid DescriptionA neuronal ceroid lipofuscinosis that is characterized by autosomal recessive inheritance with adult onset of progressive cognitive decline and motor dysfunction leading to dementia and often early death and has_material_basis_in homozygous or compound heterozygous mutation in the CTSF gene on chromosome 11q13.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_15958
Doid IdDOID_0110727
LabelNeuronal Ceroid Lipofuscinosis 13