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Neuronal Ceroid Lipofuscinosis 6A

Disease ID: disease_node_15956

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DbxrefGARD:1224, ICD10CM:E75.4, MIM:601780, ORDO:228363
SubclassofDOID_0050737, DOID_14503
Data SourceDOID
SynonymsCLN6, neuronal ceroid lipofuscinosis 6, neuronal ceroid lipofuscinosis 6 variable age of onset
Doid Labelneuronal ceroid lipofuscinosis 6A
Doid DescriptionA neuronal ceroid lipofuscinosis that is characterized by progressive decline of neurologic function, including visual deterioration in most, cognitive impairment, loss of motor function, and seizures and has_material_basis_in homozygous mutation in the CLN6 gene on chromosome 15q21-q23.
Existence Starts DuringHP_0011463
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_15956
Doid IdDOID_0110729
LabelNeuronal Ceroid Lipofuscinosis 6A