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Neuronal Ceroid Lipofuscinosis 4

Disease ID: disease_node_15951

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DbxrefICD10CM:E75.4, MIM:162350, ORDO:228343
SubclassofDOID_0050736, DOID_14503
Data SourceDOID
SynonymsCLN4B disease, autosomal dominant neuronal ceroid lipofuscinosis 4B, neuronal ceroid lipofuscinosis 4 Parry type, neuronal ceroid lipofuscinosis 4B
Disease Has FeatureDOID_0080831, DOID_0050753
Doid Labelneuronal ceroid lipofuscinosis 4
Doid DescriptionA neuronal ceroid lipofuscinosis that is characterized by autosomal domit inheritance, onset of symptoms (psychiatric manifestations, seizures, cerebellar ataxia, and cognitive decline) in adulthood and has_material_basis_in heterozygous mutation in the DNAJC5 gene on chromosome 20q13.
Has SymptomSYMP_0000124
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_15951
Doid IdDOID_0110720
LabelNeuronal Ceroid Lipofuscinosis 4