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Multiple Synostoses Syndrome 1

Disease ID: disease_node_15745

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DbxrefGARD:3836, MIM:186500
SubclassofDOID_0050794
Data SourceDOID
Doid Labelmultiple synostoses syndrome 1
Doid DescriptionA multiple synostoses syndrome is characterized by multiple joint fusions, usually commencing in the hands, conductive deafness, and characteristic facial features, including a broad, tubular-shaped nose and a thin upper vermilion and that has_material_basis_in heterozygous mutation in the NOG gene on chromosome 17q22.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_15745
Doid IdDOID_0081317
LabelMultiple Synostoses Syndrome 1