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Multiple Synostoses Syndrome 3

Disease ID: disease_node_15743

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DbxrefMIM:612961
SubclassofDOID_0050794
Data SourceDOID
Doid Labelmultiple synostoses syndrome 3
Doid DescriptionA multiple synostoses syndrome that is characterized by multiple joint fusions, usually commencing in the hands, conductive deafness, and characteristic facial features, including a broad, tubular-shaped nose and a thin upper vermilion and that has_material_basis_in heterozygous mutation in the FGF9 gene on chromosome 13q12.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_15743
Doid IdDOID_0081319
LabelMultiple Synostoses Syndrome 3