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Nager Acrofacial Dysostosis

Disease ID: disease_node_15739

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DbxrefGARD:498, MIM:154400, NCI:C35795, UMLS_CUI:C1332140
SubclassofDOID_0060379
Data SourceDOID
SynonymsAFD, Nager syndrome, acrofacial dysostosis 1, Nager type, preaxial acrofacial dysostosis, preaxial manibulofacial dysostosis
Doid LabelNager acrofacial dysostosis
Doid DescriptionAn acrofacial dysostosis characterized by underdeveloped cheek bones, very small lower jaw, cleft palate, defects in the middle ear, absent eyelashes, and a notch in the lower eyelids called a coloboma, in children. OMIM mapping confirmed by DO. [SN].
Disease Node Iddisease_node_15739
Doid IdDOID_5768
LabelNager Acrofacial Dysostosis