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Frontometaphyseal Dysplasia 1

Disease ID: disease_node_15703

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DbxrefMIM:305620
SubclassofDOID_0080012, DOID_0111785
Data SourceDOID
SynonymsFMD1
Doid Labelfrontometaphyseal dysplasia 1
Doid DescriptionA frontometaphyseal dysplasia characterized by generalized skeletal dysplasia, deafness, and urogenital defects that has_material_basis_in homozygous or hemizygous mutation in FLNA on chromosome Xq28.
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_15703
Doid IdDOID_0111786
LabelFrontometaphyseal Dysplasia 1